DOI: 10.36347/sjams.2021.v09i05.002

Pages: 636-639

Unilateral agenesis of the pulmonary artery is a rare congenital cardiovascular malformation (1% of congenital heart diseases), it can be isolated or associated with different congenital heart diseases. We report the case of a young patient aged 18, operated on in childhood for congenital heart disease without document, admitted to resuscitation unit for heart failure. After stabilization of the patient's hemodynamic status, a thoracic CT angiography (done as part of the etiological assessment) was performed showing agenesis of the left pulmonary artery, left brachiocephalic artery and a permeable blalock-tausing shunt between the brachiocephalic artery and the trunk of the pulmonary artery which is reduced in size with direct emergence of the arch of the aorta the right subclavian artery and the right common carotid. The patient remained hemodynamically stable with 60% ambient air saturation.