DOI: 10.36347/sjmcr.2021.v09i05.007

Pages: 493-496

Desmoid tumors also called fibromatosis of the face are very rare especially in children. These tumors although benign are known to be reccurent and very aggressive locally so they can be confused with malignant tumors. Several treatments can be offered, but only surgery with a complete excision remains the guarantee of a complete remission. Case report: We present a case of mandibular desmoid tumor in a 2-year-old girl who presented with left mandibular mass rapidly increasing in volume. After the biopsy has confirmed the nature of the tumor, surgical treatment has been proposed thus proceeding with the complete excision of the tumor. The postoperative follow-up was simple. No recurrence was recorded 2 years after the operation. Conclusion: The treatment of a desmoid facial tumor in children is difficult, all the more so as the tumor is large or locally aggressive. Wide excision is the only guarantee of a good evolution even if it can compromise the growth potential.