DOI: 10.36347/sasjm.2021.v07i10.014

Pages: 576-578

Sturge-Weber syndrome (SWS) or encephalofacial angiomatosis is a rare neurocutaneous and congenital ocular syndrome. It is responsible about two malformations: congenital facial capillary planar angioma and leptomeningal venous-capillary angioma (most often parieto-occipital homolateral angioma). Neuroimaging, especially magnetic resonance imaging (MRI), makes the diagnosis, ideally before ocular complications. In Sturge-Weber syndrome neurodevelopmental outcomes depend to accurate recognition of the signs of severity and proper therapeutic management of epilepsy. We report the case of an old man in whom SWS was suspected based on facial angioma and epilepsy.