DOI: 10.36347/sjmcr.2021.v09i11.004

Pages: 1059-1061

Synovialosarcoma is a rare malignant tumor, accounting for 10% of soft tissue sarcomas. It usually develops in the limbs and its pulmonary location is exceptional. We report a clinical case of synovialosarcoma of the lung in a 65-year-old man discovered at a localized stage. This extremely rare tumor has a particular immunohistochemical phenotype, which greatly contributes to the diagnosis. The cytogenetic study confirms the diagnosis by showing the presence of the specific translocation t (X; 18), which characterizes the synovialosarcoma whatever its anatomical location. Through this observation, we insist on the radiology-clinical, therapeutic and prognostic characteristics of this rare tumor often unrecognized by clinicians.