DOI: 10.36347/sasjm.2022.v08i01.004

Pages: 13-16

The pediatric adrenocortical carcinoma is a rare cancer estimated at 0.3-0.38 cases per million children per year. its diagnosis is based on a set of clinical, biological and radiological arguments. Its rarity, coupled with a relatively poor literature, especially from a prospective point of view, make the therapeutic approach to this cancer a real challenge. This work identifies 6 patients who were treated in the pediatric surgery department A of the children's hospital in Rabat over a period of 28 years, and aims to shed light on the various clinical, biological and radiological aspects of malignant adrenocortical carcinoma, as well as different therapies used and the outcome of these children; and offers a comparative approach with what the literature offers.