DOI: 10.36347/sasjs.2022.v08i05.004

Pages: 351-353

Malignant peripheral nerve sheath tumors or MPNST are rare tumors and the main complication of neurofibromatosis type1. MPNST is most common in young adults and middle-aged adults. They occur mainly in the roots of the limbs and trunk and less frequently in the head and neck. MRI is the examination of choice in this type of tumor. The diagnosis is histological. The main treatment is surgery and the adjuvant treatment is indicated to prevent any recurrence. We report a very rare case of MPNST tumor of the nasal cavity and we will underline through this work the aggressiveness and the unpredicted prognosis of this malignant tumor.