DOI: 10.36347/sjmcr.2014.v02i01.017

Pages: 42-44

Sclerosing epithelioid fibrosarcoma is an unusual variant of fibrosarcoma composed of bland epithelioid cells deposited in a densely hyalinised collageneous matrix.A 41 year male patient admitted with complains of pain in right hip since 6 months. He was a known case of fibrosarcoma (soft tissue) operated 3 years ago. On examination, old scar on medial aspect of right thigh was seen. Tenderness was present over right greater trochanter. A biopsy was performed which was diagnosed as Sclerosing epithelioidfibrosarcoma.Sclerosing epithelioidfibrosarcoma is a rare, slow growing, sarcoma of deep soft tissue with bland epithelioid tumor cells in nests and cords set in hyalinized fibrous stroma. As it is a clinically aggressive but histologically low-grade sarcoma with unsatisfactory treatment results and also has a high recurrence rate with high metastatic potential, it is important to consider this rare entity as a possible differential diagnosis in all suspicious soft tissue sarcomas.