DOI: 10.36347/sjmcr.2020.v08i02.038

Pages: 241-242

Schizencephaly is a malformation of the central nervous system related to the presence of an extended unilateral or bilateral cleft of the lateral ventricle on the surface of the cerebral cortex. This is a retrospective and descriptive study of 16 cases of schizencephaly collected over a period of 8 years (January 2011 to December 2019). A radiological assessment made of a brain scan performed in 11 patients and a cerebral MRI performed in 5 patients. The reported cases ranged in age from 2 months to 45 years with a male predominance and a sex ratio of 1.66. The clinical symptomatology was dominated by epileptic seizures, psychomotor retardation and motor deficit. The malformations were divided as follows: unilateral schizencephaly (15 cases: 6 type I and 9 type II) and bilateral schizencephaly (1 case: type II). Schizencephaly is an uncommon cerebral malformation that is most often revealed by epilepsy. It is characterized by a cleft with open or closed lips sitting most often in the Rolandic regions. Imaging, especially MRI, is essential in the positive diagnosis and the assessment of lesions.