DOI: 10.36347/sjmcr.2020.v08i03.043

Pages: 410-416

Aortopulmonary window (APW) is an uncommon congenital cardiac malformation, accounting for 0.1% of all congenital cardiac diseases. It results from an incomplete division between the ascending aorta and the pulmonary artery. Clinical and hemodynamic presentation of this condition depends on the size of the defect and on the associated lesions. It is usually fatal in infancy or childhood if untreated with the development of irreversible pulmonary hypertension. Very few cases of those who have survived to adulthood have been described. Herein, we report the case of a 42-year-old female patient who presented with an Eisenmenger syndrome and pulmonary hypertension that she first declared at the age of 39-years-old, with special attention to clinical, echocardiographic and angiographic data, leading us to a diagnosis of APW associated with PDA.