DOI: 10.36347/sjmcr.2020.v08i03.045

Pages: 421-423

A 12 years old girl admitted in Bangabandhu Sheikh Mujib Medical University (BSMMU) with the complaints of occasional abdominal pain, vomiting and a mass in abdomen for four months. Her physical examination revealed a large solid mass measuring about 10x8 cm in left hypochondriac and epigastric region, CT scan of abdomen revealed mass was pancreatic in origin. Surgery was done and during exploration the mass was nodular, capsulated and cut surface was solid with necrotic and haemorrhagic areas, histopathology report was pancreatoblastoma and there was capsular and perineural invasion. She completed adjuvant chemotherapy and was on follow up but after two years she died due to local recurrence. Pancreatoblastoma (PB) is a rare childhood malignancy of pancreatic islet cells and so far our knowledge goes it is one of the few cases diagnosed in Bangladesh. In most cases tumor is located in the head of the pancreas and patients usually presents with abdominal pain and mass, vomiting, diarrhea or jaundice. The presenting features are non-specific, so it is difficult to distinguish from other inra-abdominal tumors. Here, we describe the diagnosis, clinical and histological characteristics of the tumor, and the management.