DOI: 10.36347/sjmcr.2014.v02i03.033

Pages: 214-216

Progressive hemifacialatrophy ,also known as Parry-Romberg syndrome, is an uncommon, degenerative and poorly understood condition. It is characterized by a slow and progressive atrophy affecting one side of the face ,generally left . An autoimmune mechanism is suspected and the syndrome may be a variant of localized scleroderma .A cerebral disturbance of fat metabolism has been proposed as a primary cause . This can be result of a atrophic malformation of cerebral sympathetic nervous system. Possible factors that are involved in the pathogenesis are trauma, viral infections ,heredity, endocrine disturbances ,and autoimmunity ,among others. Characteristically, atrophy progresses slowly for several years and, soon after, it become stable. The purpose of this work is to report a clinical case with right sided progressive hemi facial atrophy and affecting a middle age group male which itself is a rare presentation of this uncommon condition.