DOI: 10.36347/sjmcr.2022.v10i10.011

Pages: 1034-1039

Background: Uterus didelphys with blind hemivagina Ipsilateral renal agenesis (Herlyn Werner Wunderlich Syndrome) is a rare congenital anomaly. The true incidence of this anomaly is unknown, but it has been reported between 0.1% and 3.8%. Another name is “Double uterus-hemivaginal-renal agenesis syndrome." Case Summary: We present the case of Uterus didelphys with hemivagina with ovarian endometrioma ē Ipsilateral renal agenesis in a 14- year-old girl. Patient was symptomatically treated. She was then referred to BSMMU on 28-02-22 for further management. Conclusion: Neglected and inappropriately managed Uterus didelphys with hemivagina with ovarian endometrioma ē Ipsilateral renal agenesis can lead to endometriosis and infertility.