DOI: 10.36347/sjmcr.2014.v02i10.010

Pages: 674-676

Rhabdomyosarcoma(RMS) is the most common soft tissue sarcoma in children and frequently involves the head and neck region with 10% of the cases primarily involving the orbit. It is a highly malignant tumor which can be life threatening. CT and MRI are important in the evaluation of this tumor. Histologically, embryonal subtype is the commonest in children. Complete resection followed by chemotherapy and radiotherapy is the preferred treatment of choice. We report a case of Embryonal Rhabdomyosarcoma of Orbit presenting with rapid proptosis of right eye in a 13 year old female child.