DOI: 10.36347/sjmcr.2015.v03i04.011

Pages: 319-322

Synovial sarcoma [SS] is a very rare soft tissue tumor accounting for 5.6 to 10% of all soft tissue sarcomas. Approximately 9% synovial sarcomas occur in head and neck region. SS is highly aggressive in nature and has tendency for distant metastasis. Most common site for head and neck synovial sarcoma is hypo pharynx, post pharyngeal region and parapharyngeal space. Very few cases of SS involving tongue, soft palate, mandible, buccal mucosa, and floor of the mouth have been described in the literature. Based on extensive literature review, very few cases of primary synovial sarcoma of mandible were noted in the literature .Here, we report a rare case of primary synovial sarcoma arising from mandible in a 40 year old lady and treated with definitive surgery.