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Scholars Journal of Medical Case Reports | Volume-3 | Issue-04
Non Functional Retroperitoneal Paraganglioma Presenting with Extensive Skeletal Disease: A Case Report and Review of Literature
Channabasappa Kori, Shashi Singh Thakur, Vijay Kumar, Sameer Gupta, Neelesh Jain, Parijat Suryavanshi
Published: April 30, 2015 | 92 68
DOI: 10.36347/sjmcr.2015.v03i04.020
Pages: 351-354
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Abstract
Paragangliomas (PGs) are very rare extra adrenal tumors derived from neuroendocrine cells of autonomic nervous system which rarely present as retroperitoneal mass. The Extra-adrenal paragangliomas are reported to account for only 10-15% of all paragangliomas. They may present incidentally as a mass. Histological findings are used for definitive diagnosis and surgery is the treatment of choice. We report a case of a non functional retroperitoneal PG with extensive skeletal metastasis in a 22-year-old gentleman treated with palliative chemotherapy.