DOI: 10.36347/sjds.2015.v02i04.006

Pages: 290-292

Abstract: Gorlin-Goltz syndrome which is also known as Bifid rib syndrome comprises of multiple organ system. One of the most common features includes the multiple odontogenic keratocysts in maxilla or mandible and basal cell nevus on the skin that usually shows an early age onset. Studies have showed that Gorlin syndrome is an autosomal dominant disorder which arises from chromosome defects. These multiple odontogenic keratocysts should be treated at the earliest for the related damage and possible complications associated. One thing that should be taken in consideration while explaining the prognosis to the patient is the recurrence of these lesions which is the most characteristic feature. A case report of a young female patient with Gorlin-Goltz syndrome is presented here.