DOI: 10.36347/sjams.2015.v03i02.085

Pages: 962-965

Nasal glial heterotopias (NGH) are rare nonhereditary congenital malformations composed of heterotopic neuroglial tissue. Congenital midline nasal masses are rare and have been reported to occur in 1 in 20000-40000 livebirth. NGH accounts for 5% of them. NGH usually presents during infancy but occasionally in older children and adults. Evaluation should be done with CT scan & MRI to rule out intracranial extension. There have been several cases reported in which NGH were misdiagnosed as capillary hemangiomas, dermoid cyst, teratoma, encephaloceles and even desmoids. A near definitive diagnosis can be carried out by following a proper clinical, sonological and including CT, MRI evaluation, while surgical excision and histopathological confirmation is of gold standard. We report a rare case of midline 3×3×3cm firm, subcutaneous, non-tender, non-pulsatile, non-compressible, non-reducible with posture and pressure swelling, covered with bluish red skin at root of nose. On CT scan and MRI swelling was given differential diagnosis of encephalocele, NGH and dermoid. It was histopathology which gave definitive diagnosis of NGH. The case represents importance of histopathology as gold standard in diagnosis of NGH.