DOI: 10.36347/sjmcr.2020.v08i07.017

Pages: 714-722

Aim: Determine the epidemiological, radiological, therapeutic and progressive profile of bronchopulmonary malformations. Materials and methods: This is a retrospective study over 10 years (03/2010 to 10/2019), including 20 children hospitalized in our institution for bronchopulmonary malformation. Results: We have identified 7 cases of adenomatoid cystic lung malformations, 3 cases of congenital lobar emphysema,3 cases of pulmonary sequestration in its extra lobar form, 3 cases of bronchogenic cyst, 1case of pulmonary sequestration associated with cystic adenomatoid malformations, 1 case of Pulmonary hypoplasia, 1 case of pulmonary agenesis and 1 case of pulmonary arteriovenous malformation. The prenatal diagnosis was carried out in a single patient, other patient benefited from a postnatal diagnosis with an average age of 26 months. All patients were symptomatic with an average age of 14 months. The symptomatology was dominated by respiratory distress, and respiratory infection. The chest X-ray guided the diagnosis in most cases and the CT scan confirmed the diagnosis of all cases. Lobectomy was performed in 67% of the patients. The pathological examination confirmed the diagnosis of the malformation in all cases. The post-operative and long-term outcome, with a follow-up ranging from 3 months to 3 years, was favorable in most of the patients followed. Conclusion: Imaging has a fundamental role in the management of congenital pulmonary malformations, in their diagnosis and in the assessment of surgical forms. CT is the modality of choice, thanks to its ease of access, its speed of acquisition, its high spatial resolution that it offers.