DOI: 10.36347/sjmcr.2020.v08i09.004

Pages: 823-824

Charcot-Marie-Tooth disease (CMTD) is a hereditary peripheral neuropathy and is characterized by progressive muscle atrophy and motor-senrory disorders in all 4 limbs. A 27-year- old man was scheduled to undergo endoscopic sinus surgery, septoplasty and turbinoplasty due to chronic paranasal sinusitis, deviated septal nose and both chronic hypertrophic rhinitis. He had been diagnosed with Charcot-Marie-Tooth disease in 2008. General anesthesia was induced with propofol 120 mg and the intubating condition was achieved with rocuronium 50 mg. Anesthesia was maintained with 1.5-2% sevoflurane and remifentanil. During surgery, the body temperature and end tidal concentration of CO2 were maintained within the normal range. Despite the continuous monitoring of the train-of-four (TOF) response, no more muscle relaxants were required during surgery and the patient recovered with suggamadex 200mg and the patient awaked without a delay. In the management of patients with Charcot-Marie-Tooth disease, it is desirable to evaluate the patient carefully, select the appropriate anesthetics and adjust the dosage of the drug according to the patients requirements.