DOI: 10.36347/sjmcr.2020.v08i10.012

Pages: 911-914

Aortopulmonary window (APW) is a rare congenital cardiac anomaly.These malformations originate an important left-right shunt with congestive heart failure in the first days or months of life, and early development of severe pulmonary hypertension.7 Until the present, only about 300 cases have been published; for the most part as isolated reports.3-5We report our experience with surgical treatment of APW in 2 consecutive patients in the first years of life. Two infants respectively 4 years old male, 6-month-old male have been referred to our hospital with a medical history of dyspnea, tachypnoea without cyanosis and history of recurrent pulmonary infections. There was no perinatal illness in both infants. An APW diagnostic was performed byechocardiography and type I was identified. The anatomical defects have been repaired surgically using synthetic patch and autologous pericardial patch according to the anatomical type. Additional gests were also performed. The surgical procedures were uneventful. Post-operative course was favourable in one infant with best post-operative recovery. However one infant deceased in day 10 post-operative due to sepsis chock. In conclusion surgical repair is the gold standard of the treatment of APW with good results. Due to the irreversible pulmonary vascular disease this malformation should be diagnosed early and repaired at the diagnosis.