DOI: 10.36347/sjams.2016.v04i06.003

Pages: 1881-1883

Isolated Partial Anomalous Pulmonary Venous Connection is a rare congenital defect that may not clinically manifest until adulthood. It can be misdiagnosed as a secundum type atrial septal defect by an echo cardiographer too. We present a 9 year-old girl who presented to us with complaints of occasional exertional fatigue. An ejection systolic murmur was heard in the 2rd inter-costal space at left parasternal area. The cardiothoracic ratio was normal in routine chest X-ray with an anomalous vessel adjacent to the left pulmonary hilum. Echocardiography revealed an ostium secondum type of atrial septal defect of 18x10 mm in size with absence of inferior limb. She was taken up for surgery for closure of atrial septal defect. Intraoperatively, it was found that the atrial septum was intact but the right inferior pulmonary vein was draining to the right atrium. Surgically the defect was corrected by resecting part of atrial septum and tunneling the right inferior pulmonary vein to left atrium with a Dacron patch. The postoperative outcome was uneventful.