DOI: 10.36347/sjmcr.2015.v03i05.002

Pages: 359-363

Cleidocranial dysplasia is a developmental anomaly of the skeleton and the teeth which is result of faulty development of membranous bones. This condition may be inherited or transmitted as dominant characteristics in either sex, or even may appear spontaneously. It presents with a wide range of features, characterized by clavicular aplasia or hypoplasia, short stature, supernumerary teeth. Other features include skeletal abnormalities like skeletal defects of several bones, such as late closure of the fontanels, presence of open skull sutures and multiple wormian bones. The clavicular abnormality ranges from a small defect in one clavicle to complete absence of both. Clinical significance of this condition to dentistry is due to the involvement of the facial bones, altered eruption patterns and multiple supernumerary teeth. Here presenting case of 25-year-old Indian male, presented with the typical features of prolonged retention of deciduous dentition and impacted permanent teeth, mandibular prognathism along with other skeletal abnormalities like shrugged shoulder and the absence of clavicles.