DOI: 10.36347/sjmcr.2016.v04i04.010

Pages: 212-215

A 7 1/2 month female child came with features of abdominal distension along with fever and frequency of micturition. Child was operated outside for similar complaints two months back. Examination revealed single opening in the introitus with postaxial polydactyly with syndactyly. Investigations including USG and CT abdomen showed cystic lesion behind the bladder. Abdominal exploration after genitoscopy revealed pyometrocolpos with high vaginal atresia. A temporary vaginostomy was done. We present a delayed presentation of McKusick Kaufman syndrome.