DOI: 10.36347/sasjs.2023.v09i04.009

Pages: 252-260

Introduction: Caroli disease is rare congenital disorder characterized by segmental intrahepatic bile duct ectasia always communicating with the bile ducts. Methods: The aim of this study for 08 cases of Caroli disease is to assess the role of surgery in the treatment of Caroli disease unilubar, focusing on epidemiological, clinical, anatomopathological and surgical aspects. Results: The middle age was 52,24 years with (4H/4F), this disease was located on the left in 7 cases and on the right in one case. It was manifested by abdominal pain (100%), cholangitis (25%), jaundice (25%) and fever (12,5). It was complicated by intrahepatic lithiasis (75%), liver abscess (27,5%) and cholangiocarcinoma (25%). Hepatic cholestasis was found in 3 cases. Imaging evoked the diagnosis by showing cystic dilatation of the intrahepatic bile ducts communicating with the biliary tree. Hepatic resection was the treatment of choice for 7 patients with bilio-digestive anastomosis on Y in 2 patients and a lateral-lateral choledoco-duodenal bypass in 2 patients. Histology confirmed the diagnosis in all cases. Two patients died 1 month after the procedure. Only one patient was lost to follow-up and the evolution was favorable for the other patients with a mean follow-up of 6 years. Conclusions: It seems evident that premature treatment followed by regular supervision makes it possible to detect and treat complications.