DOI: 10.363247/sjmcr.2018.v06i10.033

Pages: 865-868

Malignant peripheral nerve sheath tumors (MPNST) are considered a rare entity, especially in the retro peritoneum. We report the case of a 32 years old woman, with the history of Von Recklinghausen disease, who presented a MNPST of 14,5 cm of diameter at the retroperitoneal cavity. There was no specific clinical symptom besides an abdominal swelling. The MRI showed a heterogeneous retroperitoneal mass that represses without invading the adjacent structures. We’ve conducted a mass resection without any adjuvant radio or chemotherapy. No sign of local recurrence was detected after one year follow up.