DOI: 10.36347/SJMCR.2019.v07i10.006

Pages: 614-618

Prune Belly Syndrome (PBS) or Eagle-Barrett Syndrome is a congenital disorder that typically associates aplasia or hypoplasia of the anterior wall muscles of the abdomen, urinary malformations, and bilateral cryptorchidism. Other malformations such as pulmonary, skeletal, cardiac and gastrointestinal malformations may also be associated. Antenatal diagnosis can be done by echography. We report the case of a 32-year-old patient, referred in our formation at the CHU Hassan II of Fez at 24SA for a severe oligoamnios. Obstetrical ultrasound showed a bilaterally uretral pyelocaliciel dilatation associated with mega-bladder and dilatation of the ureter in a male fetus. An abnormality of the anterior abdominal wall was suspected with an ultrasound appearance suggestive of agenesis of the right muscles of the abdomen. The plum belly syndrome has been suspected. The patient presented a premature delivery at 32SA. Examination of the new born finds a thin, flaccid, wrinkled skin appearance, with empty purses. NN died from respiratory distress 2 hours after delivery. We discussed through this observation the various malformations found in Belly Prune Syndrome, the prenatal and postnatal ultrasound diagnosis, the fate of these children and their therapeutic management.