DOI: 10.36347/sjmcr.2021.v09i03.001

Pages: 197-201

Introduction: Atypical aortic coarctation is very rare, accounting for up to 2 % of aortic coarctation malformation. Several etiologies have been described and the most common is the Takayasu’s arteritis. Skin manifestations of TA are very rare and an association with pyoderma gangrenosum has been reported. This case highlights the diagnosis and management challenges. Case report: A 10 years old boy with pyoderma gangrenosum was admitted for hypertensive emergency. TEE and CT scan further revealed an atypical aortic coarctation complicating Takayasu arteritis. The inflammatory storm was managed with immunosuppressive therapy. Conclusion: Atypical aortic coarctation is rare. Takayasu’s disease is its main reported etiology and has poor prognosis. Early diagnosis and treatment are therefore crucial to prevent further damage to the blood vessel.