DOI: 10.36347/sjmcr.2020.v08i02.031

Pages: 219-221

Persistent mullerian duct syndrome is a disorder of sexual development that commonly affects male, also known as Hernia uteri inguinale. They have male external genitalia with admixture of male and female reproductive organs. Common clinical presentation is with infertility or inguinal hernia. The main modality of therapy is surgery. Early diagnosis and therapy maintains fertility and prevents malignant change. We are reporting a case of persistent mullerian duct syndrome in a 40 year old male who presented with inguinal hernia with preserved fertility.