DOI: 10.36347/sjmcr.2014.v02i06.016

Pages: 401-404

Congenital midline swellings of nose are encountered rarely, and nasal gliomas constitute about 5% of such lesions. Nasal gliomas are rare, benign, developmental abnormality of neurogenic origin, generally sporadic, with no familial tendency and are thought to be the result of an error in embryonic development. They are typically slow growing and very rarely associated with other congenital malformations. Extranasal gliomas are usually located at the glabella level, but may present laterally. High-resolution MRI is often useful in demonstrating intracranial stalk. Complete surgical excision of the tumor is the treatment of choice. Etiology of unilateral cleft nasal deformity is a lack of skeletal support of the cleft alar base. Early management of the nasal deformity minimizes nasal asymmetries and allows the nose to grow in a symmetric fashion. We present an infrequent case of nasal glioma associated with unilateral nasal cleft in a five month old child.